Unusual Presentation in Infratentorial Superficial Siderosis: Acute Intracranial Hypertension
Unusual Presentation in Infratentorial Superficial Siderosis: Acute Intracranial Hypertension
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Superficial siderosis (SS) of the nervous system is a rare acquired condition related to princess jasmine silhouette hemosiderin deposits in subpial layers of the brain, brainstem, cerebellum, cranial nerves, and spinal cord, leading to brain iron-mediated neurodegeneration.The cardinal neurological features are slowly progressive hearing loss, ataxia, and pyramidal signs.Here we describe an atypical case of infratentorial SS evolving with acute intracranial vince camuto fiori gift set hypertension in the absence of typical chronic signs.
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